{"id":275,"date":"2025-03-26T12:53:38","date_gmt":"2025-03-26T11:53:38","guid":{"rendered":"https:\/\/www.neuromuscularbcn.org\/?page_id=275"},"modified":"2025-04-29T10:36:31","modified_gmt":"2025-04-29T08:36:31","slug":"assistencia","status":"publish","type":"page","link":"https:\/\/www.neuromuscularbcn.org\/ca\/assistencia\/","title":{"rendered":"Assist\u00e8ncia"},"content":{"rendered":"<div class=\"fusion-fullwidth fullwidth-box fusion-builder-row-1 fusion-flex-container has-pattern-background has-mask-background nonhundred-percent-fullwidth non-hundred-percent-height-scrolling\" style=\"--awb-border-radius-top-left:0px;--awb-border-radius-top-right:0px;--awb-border-radius-bottom-right:0px;--awb-border-radius-bottom-left:0px;--awb-flex-wrap:wrap;\" ><div class=\"fusion-builder-row fusion-row fusion-flex-align-items-flex-start fusion-flex-content-wrap\" style=\"max-width:1422.72px;margin-left: calc(-4% \/ 2 );margin-right: calc(-4% \/ 2 );\"><div class=\"fusion-layout-column fusion_builder_column fusion-builder-column-0 fusion_builder_column_1_1 1_1 fusion-flex-column cnt_PagGen_Content_col\" style=\"--awb-bg-size:cover;--awb-width-large:100%;--awb-margin-top-large:0px;--awb-spacing-right-large:1.92%;--awb-margin-bottom-large:0px;--awb-spacing-left-large:1.92%;--awb-width-medium:100%;--awb-order-medium:0;--awb-spacing-right-medium:1.92%;--awb-spacing-left-medium:1.92%;--awb-width-small:100%;--awb-order-small:0;--awb-spacing-right-small:1.92%;--awb-spacing-left-small:1.92%;\" data-scroll-devices=\"small-visibility,medium-visibility,large-visibility\"><div class=\"fusion-column-wrapper fusion-column-has-shadow fusion-flex-justify-content-flex-start fusion-content-layout-column\"><div class=\"fusion-text fusion-text-1\"><p><img decoding=\"async\" class=\"size-full wp-image-2694 alignnone\" src=\"https:\/\/www.neuromuscularbcn.org\/wp-content\/uploads\/2025\/04\/article-1.jpg\" alt=\"\" width=\"620\" height=\"220\" srcset=\"https:\/\/www.neuromuscularbcn.org\/wp-content\/uploads\/2025\/04\/article-1-200x71.jpg 200w, https:\/\/www.neuromuscularbcn.org\/wp-content\/uploads\/2025\/04\/article-1-300x106.jpg 300w, https:\/\/www.neuromuscularbcn.org\/wp-content\/uploads\/2025\/04\/article-1-400x142.jpg 400w, https:\/\/www.neuromuscularbcn.org\/wp-content\/uploads\/2025\/04\/article-1-600x213.jpg 600w, https:\/\/www.neuromuscularbcn.org\/wp-content\/uploads\/2025\/04\/article-1.jpg 620w\" sizes=\"(max-width: 620px) 100vw, 620px\" \/><\/p>\n<p>La unitat de Malalties Neuromusculars (UMNM) del Servei de Neurologia del Hospital de Sant Pau (HSCSP), dedica la seva atenci\u00f3 assistencial a les malalties del Sistema Nervi\u00f3s Perif\u00e8ric ( m\u00e8dul.la espinal, arrels, nervi perif\u00e8ric, uni\u00f3 neuromuscular i m\u00fascul). Aquestes malalties s\u00f3n d\u2019etiologia diversa, per\u00f2 tenen en com\u00fa que pel seu diagn\u00f2stic i tractament s\u2019utilitzen una s\u00e8rie d\u2019exploracions i proves complement\u00e0ries molt espec\u00edfiques i d\u2019alta complexitat, tant d\u2019aprenentatge com de maneig cl\u00ednic i terap\u00e8utic.<\/p>\n<h4>JUSTIFICACI\u00d3 DE LA UENMR \u2013 HSCSP<\/h4>\n<p>Aquesta unitat es va iniciar en el seu concepte actual al 1992, i es justifica per una s\u00e8rie de motius que inclouen:<\/p>\n<ol>\n<li>Les Malalties Neuromusculars s\u00f3n un grup de malalties perfectament identificables dins de la Neurologia. Es reconeix com una \u00e0rea d\u2019especialitzaci\u00f3 despr\u00e9s d\u2019acabar la formaci\u00f3 de Neurologia.<\/li>\n<\/ol>\n<ol start=\"2\">\n<li>Una part important d\u2019aquestes malalties tenen una incid\u00e8ncia i\/o prevalen\u00e7a que les qualifica com malalties minorit\u00e0ries. No obstant aix\u00f2, el n\u00famero de patologies neuromusculars diferents \u00e9s ampli, el que significa que a la poblaci\u00f3 hi ha un n\u00famero elevat d\u2019afectats. Impliquen, tamb\u00e9, un gran impacte tant personal, com familiar i social. Entre aquestes malalties trobem l\u2019esclerosis lateral amiotr\u00f2fica (ELA), les neuropaties heredit\u00e0ries o immunomediades (S. Guillain-Barr\u00e9, CIDP i altres), la miast\u00e8nia gravis (MG), les distr\u00f2fies musculars o les miopaties inflamat\u00f2ries entre altres.<\/li>\n<\/ol>\n<ol start=\"3\">\n<li>Els m\u00e8todes diagn\u00f2stics requereixen d\u2019un aprenentatge espec\u00edfic de t\u00e8cniques comuns a totes les malalties neuromusculars (EMG, RNM\/TAC, bi\u00f2psia muscular o nervi, estudis immunol\u00f2gics o gen\u00e8tics) per\u00f2 diferents als m\u00e8todes utilitzats per la resta de patologies neurol\u00f2giques.<\/li>\n<\/ol>\n<ol start=\"4\">\n<li>Tractaments: Algunes malalties, com les immunomediades (MG, CIDP, Neuropatia motora multifocal, etc). Tenen tractament etiol\u00f2gic, per\u00f2 els tractaments s\u00f3n complexes i poden requerir ingr\u00e9s del pacient a planta o Hospital de Dia per ser medicaci\u00f3 d\u2019administraci\u00f3 endovenosa (Immunoglobulina endovenosa, ciclofosfamida, Rituximab, plasmaf\u00e8resis, etc.) \u00c9s important que siguin els neur\u00f2legs experts de la unitat els que realitzin aquests tractaments, a l\u2019estar familiaritzats no nom\u00e9s amb la malaltia sin\u00f3 amb els efectes desitjables i els efectes secundaris. D\u2019altra banda, un bon nombre de malalties neuromusculars no disposen de tractament etiol\u00f2gic, per\u00f2 \u00e9s molt important el tractament simptom\u00e0tic o de complicacions que sorgeixen durant l\u2019evoluci\u00f3 cl\u00ednica. Aquest tipus de tractament nom\u00e9s pot ser multidisciplinari i l\u2019equip que el forma, ha de con\u00e8ixer i tenir experi\u00e8ncia en aquestes malalties.<\/li>\n<\/ol>\n<h4>OBJECTIU ASSISTENCIAL DE LA UMNM-HSCSP<\/h4>\n<h6><strong>Diagn\u00f2stic i tractament dels pacients amb malalties neuromusculars<\/strong><\/h6>\n<p>L\u2019objectiu assistencial de la unitat \u00e9s proporcionar el diagn\u00f2stic i tractament integral dels pacients amb malalties neuromusculars a nivell dels est\u00e0ndards internacionals de qualitat reconeguts en cada moment.<\/p>\n<p>La vocaci\u00f3 de la unitat ha estat sempre ser centre de refer\u00e8ncia d\u2019aquestes malalties a nivell auton\u00f2mic, nacional e internacional. Amb la fi d\u2019assolir aquest objectiu la unitat ha desenvolupat una s\u00e8rie de recursos assistencials i disposa d\u2019una s\u00e8rie de recursos espec\u00edfics. Descrivim 3 nivells, el pr\u00f2piament assistencial, la realitzaci\u00f3 d\u2019estudis neurofisiol\u00f2gics i la interpretaci\u00f3 d\u2019anal\u00edtiques que s\u00f3n pr\u00f2pies del centre pel diagn\u00f2stic de MNM.<\/p>\n<h6><strong>Assist\u00e8ncia a pacients amb MNM<\/strong><\/h6>\n<p>L\u2019atenci\u00f3 als pacients amb MNM implica diferents nivells cl\u00ednics, tant hospitalari com ambulatori, aix\u00ed com consultes espec\u00edfiques multidisciplin\u00e0ries o tractaments innovadors que la UMNM ha desenvolupat al llarg dels anys.<\/p>\n<h6><strong>Estudis neurofisiol\u00f2gics<\/strong><\/h6>\n<p>La UMNM assumeix la realitzaci\u00f3 dels estudis neurofisiol\u00f2gics de la Unitat, del Servei de Neurologia i de la resta de Serveis de l\u2019Hospital de Sant Pau, aix\u00ed com dels derivats d\u2019altres centres d\u2019atenci\u00f3 prim\u00e0ria del seu entorn.<\/p>\n<h6><strong>Biomarcadors de MNM<\/strong><\/h6>\n<p>Una caracter\u00edstica de la UNMN \u00e9s traslladar\u00a0 la investigaci\u00f3 de possibles biomarcadors de patologies espec\u00edfiques, al diagn\u00f2stic cl\u00ednic.\u00a0 Hem pogut demostrar la utilitat d\u2019alguns marcadors diagn\u00f2stic s i d\u2019altres de seguiment dels pacients que ara, l\u2019HSCSP ofereix a la cartera de serveis\u00a0 en col\u2022col\u00b7laboraci\u00f3 amb els serveis d\u2019immunologia i d\u2019anatomia patol\u00f2gica.<\/p>\n<h6><strong>Assist\u00e8ncia al pacient amb MNM<\/strong><\/h6>\n<p>L\u2019assist\u00e8ncia implica els seg\u00fcents nivells:<\/p>\n<ul>\n<li>Consulta externa: nous pacients, pacients en seguiment i segones opinions<\/li>\n<li>Hospitalitzaci\u00f3<\/li>\n<li>Hospital de dia i assist\u00e8ncia urgent<\/li>\n<li>Consultes multidisciplin\u00e0ries<\/li>\n<li>Consultes monogr\u00e0fiques de MNM immunomediades<\/li>\n<li>Tractament innovadors<\/li>\n<\/ul>\n<\/div><\/div><\/div><\/div><\/div>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":3,"comment_status":"closed","ping_status":"closed","template":"100-width.php","meta":{"_acf_changed":false,"inline_featured_image":false,"footnotes":""},"class_list":["post-275","page","type-page","status-publish","hentry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.2 - 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